Cancer Commonalities: The Hallmarks of Cancer Part 2


Welcome to part 2 of our 3-part discussion on cancer commonalities!  In this series we are defining the features shared by most cancer cells as outlined in Hanahan and Weinberg’s review article.  It’s a great introduction to what defines cancer.  Let’s first recap our last discussion:  In part 1 we learned about the first 3 hallmarks of cancer: sustained proliferative signaling, evading growth suppressors, and resisting cell death.  Although distinct, these traits integrate several key signaling pathways including the Ras-MAPK pathway, the PI3K-AKT axis, and the p53 tumor suppressor pathway.  Their intricate interactions imply that alterations in one pathway can affect multiple pathways and therefore, multiple cancer traits. 



Figure 1: Hallmarks of Cancer

In today’s discussion, we will introduce the 3 remaining classical characteristics shared by cancer cells.


Enabling Replicative Immortality:
Normal cells are restricted in the number of times they can divide and pass through the cell cycle by the length of telomeres at the end of their chromosomes.  Each time a cell divides a telomere repeat is lost; and when telomeres become too short, the cell undergoes apoptosis.  Those excluded from this limitation include stem or progenitor cells, which inherently possess replicative immortality, and cancer cells which acquire the ability to divide unconditionally.  The main protein involved in maintaining the telomere is the enzyme telomerase which acts by adding telomere repeats.  Whereas this enzyme is practically absent in normal, non-immortalized cells, in cancer cells this protein is highly overexpressed and activated.  By adding telomere repeats to the end of chromosomes, it tricks the cell into passing through unlimited cell cycle passages, enabling replicative immortality.




Figure 2:  Regulation of Telomerase
Telomerase is an enzyme complex with the key functional component called hTERT.  hTERT can be transcriptionally upregulated in cancer cells through hyper-activation of specific oncogenes including AKT and c-myc or inhibited by the p53 tumor suppressor. 


Inducing Angiogenesis:
Tumors, like any other organ in the body, require oxygen and nutrients that blood carries for survival.  The ability to sprout new blood vessels, termed angiogenesis, which normally only occurs during embryonic and postnatal development, also allows an aberrant cellular mass to develop into a detectable tumor.  And like most other cellular processes, this process balances between the on/off states.  The “angiogenic switch” is governed by pro-angiogenic factors such as vascular endothelial growth factor (VEGF-A) and inhibitors including thrombospondin-1 (TSP-1).



Figure 3:  Angiogenic Switch
When cells are well oxygenated, the HIF1 protein is hydoxyenated and inactive.   Under hypoxic, or oxygen starvation, conditions such as when a tumor is growing, HIF1 translocates to the nucleus to induce transcription of growth factors and cytokines.  One of these growth factors in VEGF (Vascular Endothelial Growth Factor) which, after secretion into the extracellular matrix can bind the VEGFR receptor on neighbouring endothelial cells.  This activates downstream pathways including the AKT signaling pathway to enhance vascular permeability and vascular growth, leading to the formation of new blood vessels.  Endothelial cell signaling can be inhibited by the thrombospondin family of cell surface receptors.  The balance between vascular growth factors and thrombospondins determines the balance of the angiogenic switch.


Activating Invasion and Metastasis:
Although the growth of a primary tumor represents a diseased state, the development of metastases signals an advanced and aggressive disease and is often associated with reduced mortality.  The metastatic cascade involves a series of steps beginning with local invasion into the surrounding environment, entry of cancer cells into the blood or lymphatic systems (intravasation), transit and survival of these migrating cells in the harsh fast-flowing streams of the blood or lymphatic systems, exiting into surrounding tissue (extravasation), and finally the formation of small cancerous nodules (micrometastases) and the growth of these nodules into macroscopic lesions (colonization).  The ability of cells to undergo this process requires alterations in their morphology, most notably a change from an epithelial (densely packed, with cell-cell contacts) to a mesenchymal (migratory, elongated, and loss of cell-cell contact) phenotype.  This transition occurs mainly through activation of a transcriptional program controlled by a group of transcription factors including Snail, Slug, and Twist.  These key players orchestrate most of the metastatic cascade.


Figure 4:  Metastatic cascade (3)


Where do we go from here?

Over the last two discussions, we have defined the classical hallmarks of cancer.  Although the order in which cancer cells acquire these traits may differ, ultimately most cancer cells will share these characteristics.  For this reason, targeting a key hallmark may widely benefit cancer patients as a whole group.  This is the case with conventional chemotherapy which acts by targeting rapidly proliferating cells. 

What also becomes apparent is how cancer (and probably most disease) is a result of an imbalance.  Normal cells grow, divide, migrate, apoptose etc but under tight regulation in time and space – in other words, with the proper balance.  Cancer cells tip this balance; they carry out these same normal cellular processes, only without proper regulation.   Effective therapy aims to rebalance the cell to a homeostatic state.


References:
1        1. Hahahan D and Weinberg RA. Hallmarks of Cancer  Cell.  2001;100:57-70.
2        2. Hahahan D and Weinberg RA. Hallmarks of Cancer: The Next Generation  Cell.  2011;144:646-74.
          3. Fidler IJ.  The pathogenesis of metastasis: The ‘seed and soil’ hypothesis revisited.  Nat. Rev. Cancer. 2003;3:453-8.





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